How to perform and interpret provocative testing for the diagnosis of Brugada syndrome, long-QT syndrome, and catecholaminergic polymorphic ventricular tachycardia.
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چکیده
Manoj N. Obeyesekere, George J. Klein, Simon Modi, Peter Leong-Sit, Lorne J. Gula, Raymond Tachycardia Syndrome, Long-QT Syndrome, and Catecholaminergic Polymorphic Ventricular How to Perform and Interpret Provocative Testing for the Diagnosis of Brugada Print ISSN: 1941-3149. Online ISSN: 1941-3084 Copyright © 2011 American Heart Association, Inc. All rights reserved. Avenue, Dallas, TX 75231 is published by the American Heart Association, 7272 Greenville Circulation: Arrhythmia and Electrophysiology doi: 10.1161/CIRCEP.111.965947 2011;4:958-964 Circ Arrhythm Electrophysiol. http://circep.ahajournals.org/content/4/6/958 World Wide Web at: The online version of this article, along with updated information and services, is located on the
منابع مشابه
Advances in Arrhythmia and Electrophysiology How to Perform and Interpret Provocative Testing for the Diagnosis of Brugada Syndrome, Long-QT Syndrome, and Catecholaminergic Polymorphic Ventricular Tachycardia
Sudden cardiac death (SCD) is predominantly related to coronary artery disease and its sequelae, cardiomyopathy, and congenital or valvular heart disease. No structural abnormalities are detectable in 5–8% of SCDs.1 Identified ion channelopathies such as Brugada syndrome, long-QT syndrome (LQTS), and catecholaminergic polymorphic ventricular tachycardia (CPVT) contribute to this incidence. The ...
متن کاملSystematic assessment of patients with unexplained cardiac arrest: Cardiac Arrest Survivors With Preserved Ejection Fraction Registry (CASPER).
BACKGROUND Cardiac arrest without evident cardiac disease may be caused by subclinical genetic conditions. Provocative testing to unmask a phenotype is often necessary to detect primary electrical disease, direct genetic testing, and perform family screening. METHODS AND RESULTS Patients with apparently unexplained cardiac arrest and no evident cardiac disease (normal cardiac function on echo...
متن کاملYield of genetic screening in inherited cardiac channelopathies: how to prioritize access to genetic testing.
BACKGROUND Identification of mutations in cardiac ion channel genes concurs to the diagnosis of long-QT syndrome, Brugada syndrome, and catecholaminergic polymorphic ventricular tachycardia. However, because availability of genetic screening is still limited and reimbursement policies are lacking, there is a need of evidence-based criteria to prioritize access to genetic testing for these disea...
متن کاملGenetics of inherited primary arrhythmia disorders
A sudden unexplained death is felt to be due to a primary arrhythmic disorder when no structural heart disease is found on autopsy, and there is no preceding documentation of heart disease. In these cases, death is presumed to be secondary to a lethal and potentially heritable abnormality of cardiac ion channel function. These channelopathies include congenital long QT syndrome, catecholaminerg...
متن کاملInvited Review Role of spatial dispersion of repolarization in inherited and acquired sudden cardiac death syndromes
Antzelevitch C. Role of spatial dispersion of repolarization in inherited and acquired sudden cardiac death syndromes. Am J Physiol Heart Circ Physiol 293: H2024–H2038, 2007. First published June 22, 2007; doi:10.1152/ajpheart.00355.2007.— This review examines the role of spatial electrical heterogeneity within the ventricular myocardium on the function of the heart in health and disease. The c...
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ورودعنوان ژورنال:
- Circulation. Arrhythmia and electrophysiology
دوره 4 6 شماره
صفحات -
تاریخ انتشار 2011